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Yosuke Shigematsu Selected Research
Yosuke Shigematsu Research Topics
Disease
9
VLCAD deficiency
11/2022 - 07/2003
5
Medium chain acyl CoA dehydrogenase deficiency
09/2018 - 09/2005
5
Propionic Acidemia
09/2018 - 08/2002
4
Hypoglycemia (Reactive Hypoglycemia)
11/2015 - 08/2002
3
Citrullinemia
09/2018 - 10/2004
3
Rhabdomyolysis
01/2015 - 01/2004
3
Hyperammonemia
05/2012 - 08/2002
2
Disorders of Excessive Somnolence (Hypersomnia)
10/2022 - 12/2018
2
Narcolepsy
10/2022 - 12/2018
2
Methylmalonic acidemia
07/2021 - 10/2010
2
Trifunctional Protein Deficiency With Myopathy And Neuropathy
01/2019 - 09/2017
2
Cardiomyopathies (Cardiomyopathy)
01/2017 - 05/2012
2
Multiple Acyl Coenzyme A Dehydrogenase Deficiency
11/2014 - 02/2012
2
Intellectual Disability (Idiocy)
12/2013 - 09/2012
2
isovaleric Acidemia
10/2010 - 11/2007
2
Neonatal-onset citrullinemia type 2
05/2009 - 10/2004
2
Acute Kidney Injury (Acute Renal Failure)
03/2005 - 01/2004
1
Glutaric Acidemia I
07/2021
1
Hypermethioninemia
07/2021
1
Homocystinuria
07/2021
1
Hemophagocytic Lymphohistiocytosis (Hemophagocytic Syndrome)
01/2019
1
Fever (Fevers)
01/2019
1
Mevalonate Kinase Deficiency
01/2019
1
Cataplexy
12/2018
1
Lysinuric Protein Intolerance
10/2018
1
Ornithine Carbamoyltransferase Deficiency Disease
10/2018
1
Phenylketonurias (Phenylketonuria)
09/2018
1
Metabolic Diseases (Metabolic Disease)
09/2018
1
Sepsis (Septicemia)
03/2018
1
hypoglycemic encephalopathy
11/2017
1
Acute fatty liver of pregnancy
09/2017
1
Hemolysis
09/2017
1
Hepatomegaly
01/2017
1
Liver Neoplasms (Liver Cancer)
01/2017
1
Inborn Errors Metabolism (Inborn Errors of Metabolism)
12/2016
1
Fructose-1,6-Diphosphatase Deficiency (Fructose 1,6 Diphosphatase Deficiency)
11/2015
1
Lactic Acidosis
11/2015
1
Maple Syrup Urine Disease
09/2015
1
Adult-onset citrullinemia type 2
03/2015
1
Inborn Genetic Diseases (Disease, Hereditary)
03/2015
1
Ketosis
01/2015
1
Myoglobinuria
01/2015
1
Succinyl-CoA:3-oxoacid CoA transferase deficiency
01/2015
Drug/Important Bio-Agent (IBA)
11
Fatty Acids (Saturated Fatty Acids)
IBA
11/2022 - 08/2002
6
Long-Chain Acyl-CoA Dehydrogenase (Long-Chain-Acyl-Coenzyme A Dehydrogenase)
IBA
11/2022 - 01/2004
5
Carnitine palmitoyl transferase 2 deficiency
IBA
01/2019 - 07/2003
5
acylcarnitine
IBA
01/2019 - 07/2003
4
Carnitine O-Palmitoyltransferase (Carnitine Palmitoyltransferase II)
IBA
10/2022 - 03/2005
4
Proteins (Proteins, Gene)
FDA Link
01/2019 - 06/2010
4
Acyl-CoA Dehydrogenase (Medium-Chain Acyl-Coenzyme A Dehydrogenase)
IBA
12/2016 - 09/2005
4
Carnitine (L-Carnitine)
FDA Link
Generic
04/2014 - 08/2005
3
Acids
IBA
11/2022 - 01/2015
3
citrin
IBA
10/2018 - 10/2004
3
Enzymes
IBA
09/2017 - 07/2003
2
beta-hydroxyisovaleric acid (beta-hydroxy-beta-methylbutyrate)
IBA
07/2021 - 04/2014
2
3-methylcrotonyl CoA carboxylase 1 deficiency
IBA
07/2021 - 09/2018
2
Methionine (L-Methionine)
FDA Link
07/2021 - 10/2004
2
Carnitine palmitoyl transferase 1A deficiency
IBA
01/2019 - 07/2003
2
Amino Acids
FDA Link
09/2018 - 04/2014
2
Oxidoreductases (Dehydrogenase)
IBA
09/2015 - 11/2014
2
Creatine Kinase (Creatine Phosphokinase)
IBA
01/2015 - 01/2004
2
Anti-Bacterial Agents (Antibiotics)
IBA
10/2010 - 11/2007
1
3-hydroxyisovalerylcarnitine
IBA
07/2021
1
3-hydroxyglutaric acid
IBA
07/2021
1
Cystathionine
IBA
07/2021
1
cobamamide (adenosylcobalamin)
IBA
07/2021
1
propionylcarnitine
IBA
07/2021
1
Acetylcarnitine (Alcar)
IBA
07/2021
1
Homocysteine
IBA
07/2021
1
mevalonate kinase
IBA
01/2019
1
Transaminases (Aminotransferases)
IBA
01/2019
1
Deuterium
IBA
01/2019
1
hydroxide ion
IBA
01/2019
1
HLA-DQB1 antigen (HLA DQB1)
IBA
12/2018
1
HLA Antigens (Human Leukocyte Antigens)
IBA
12/2018
1
Carbamyl Phosphate (Carbamoyl Phosphate)
IBA
10/2018
1
Ornithine Carbamoyltransferase (Ornithine Transcarbamylase)
IBA
10/2018
1
Arginase
IBA
10/2018
1
Amino-Acid N-Acetyltransferase (N-Acetylglutamate Synthase)
IBA
10/2018
1
Ligases (Synthetase)
IBA
10/2018
1
methylcyanocarbamate dimer
IBA
09/2018
1
Procalcitonin
IBA
03/2018
1
Mitochondrial Trifunctional Protein
IBA
09/2017
1
Systemic carnitine deficiency
IBA
01/2017
1
6-propylchromone-2-carboxylic acid (PCCA)
IBA
07/2016
1
Solvents
IBA
11/2015
1
Aspartic Acid (Aspartate)
FDA Link
03/2015
1
Glutamic Acid (Glutamate)
FDA Link
03/2015
1
Antiporters
IBA
03/2015
1
Coenzyme A (CoA)
IBA
01/2015
1
Ketones
IBA
01/2015
1
Acetyl-CoA C-Acyltransferase (beta Ketothiolase)
IBA
01/2015
1
Acetyl-CoA C-Acetyltransferase (Acetyl Coenzyme A Acetyltransferase)
IBA
01/2015
1
Transferases
IBA
01/2015
1
Beta ketothiolase deficiency
IBA
01/2015
1
succinyl-coenzyme A (succinyl-CoA)
IBA
01/2015
1
Electron-Transferring Flavoproteins (Electron Transfer Flavoprotein)
IBA
11/2014
1
Bezafibrate
IBA
11/2014
1
Riboflavin (Vitamin B2)
FDA Link
Generic
11/2014
Therapy/Procedure
2
Liver Transplantation
01/2017 - 05/2012